Distal acquired demyelinating symmetric neuropathy associated with anti-GM1 antibodies: is this a CIDP variant?
نویسندگان
چکیده
Distal acquired demyelinating symmetric (DADS) neuropathy is clinically characterised by distal motor and sensory disturbances. Typically DADS does not respond or responds poorly to intravenous immunoglobulins (IVIg). We report the case of a 58-year-old patient who developed distal paraparesis. Serum electrophoresis demonstrated monoclonal IgM paraproteinemia having an anti-GM1 but no anti-MAG activity. Conduction velocities showed demyelinating pattern. Work-up excluded a lymphoproliferative disorder After IVIg treatment we observed a clinical and neurophysiological improvement. Regarding these peculiar findings, we suggest that DADS needs to be splitted in several forms determined among others by clinical, neurophysiological and antiganglioside profile and therapeutic response. We advocate to perform systematic antiganglioside antibodies assay additionnaly to anti-MAG when DADS is suspected in order to improve dysimmune neuropathies classification.
منابع مشابه
Distal acquired demyelinating symmetric neuropathy associated with anti-GM1 and anti-GD1b antibodies
is the presence of both proximal and distal weakness. Patients with both proximal and distal motor involvement are highly likely to respond to corticosteroids, irrespective of the presence or absence of a serum paraprotein. Another well-documented group of patients with symmetric, acquired, demyelinating polyneuropathies predominantly presents with sensory involvement. When weakness is present,...
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ورودعنوان ژورنال:
- Acta neurologica Belgica
دوره 110 1 شماره
صفحات -
تاریخ انتشار 2010